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    Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome

    Access Status
    Fulltext not available
    Authors
    Downs, Jennepher
    Young, D.
    De Klerk, N.
    Bebbington, A.
    Baikie, G.
    Leonard, H.
    Date
    2009
    Type
    Journal Article
    
    Metadata
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    Citation
    Downs, J. and Young, D. and De Klerk, N. and Bebbington, A. and Baikie, G. and Leonard, H. 2009. Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome. Journal of Pediatric Orthopaedics. 29 (4): pp. 369-374.
    Source Title
    Journal of Pediatric Orthopaedics
    DOI
    10.1097/BPO.0b013e3181a53b41
    ISSN
    02716798
    URI
    http://hdl.handle.net/20.500.11937/2651
    Collection
    • Curtin Research Publications
    Abstract

    Background: Scoliosis is a common orthopaedic complication of Rett syndrome, and surgery is commonly used to reduce asymmetry in cases with severe scoliosis.Methods: Data from questionnaires administered to caregivers biennially from 2000 to 2006 were used to describe functional skill levels in subjects with Rett syndrome, and within-subject change in16 subjects with scoliosis surgery were compared with within-subject change in 186 pairs of data from 86 subjects with conservatively managed scoliosis. Postsurgical assessment was conducted after amean of 17.8 months.Results: Surgery was associated with improved activities of daily living as measured by the WeeFIM for subjects who were wheelchair bound (P = 0.05). Mobility levels, social interaction, communicationskills, and the frequency of daytime napping remained similar for the group as a whole.Conclusions: Improvements in activities of daily living are likely to represent an increase in the quality of life for subjects and caregivers and were mainly found in subjects who were wheelchair bound,indicating that those who were more severely affected were able to benefit from this intervention.Level of Evidence: Therapeutic study: level III

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